MovDisordV3, France, Analysis, bibRecord, 000112

Status Dystonicus: Predictors of Outcome and Progression Patterns of Underlying Disease

Identifieur interne : 000112 ( France/Analysis ); précédent : 000111; suivant : 000113

Status Dystonicus: Predictors of Outcome and Progression Patterns of Underlying Disease

Auteurs : Alfonso Fasano [Italie] ; Lucia Ricciardi [Italie] ; Anna Rita Bentivoglio [Italie] ; Carlotta Canavese [Italie] ; Giovanna Zorzi [Italie] ; Igor Petrovic [Serbie] ; Nikola Kresojevic [Serbie] ; Vladimir S. Kostic [Serbie] ; Marina Svetel [Serbie] ; Norbert Kovacs [Hongrie] ; Istvan Balas [Hongrie] ; Agathe Roubertie [France] ; Devendra Mishra [Inde] ; Paolo Mariotti [Italie] ; Teresa Temudo [Portugal] ; Nardo Nardocci [Italie]

Source :

Movement disorders [ 0885-3185 ] ; 2012.

RBID : Pascal:12-0248755

Descripteurs français

Pascal (Inist)
- Dystonie, Pathologie du système nerveux, Pronostic, Midazolam, Pantothenate kinase.

English descriptors

KwdEn :
- Dystonia, Midazolam, Nervous system diseases, Pantothenate kinase, Prognosis.

Abstract

Background: Status dystonicus (SD) is a rare, lifethreatening disorder characterized by acute worsening of generalized dystonia. Methods: This study was conducted to characterize the pathogenesis, clinical course, and prognosis of SD. We reviewed the records of six centers and analyzed them together with all the cases previously reported in the literature. Results: Eighty-nine episodes occurring in 68 patients were studied. The majority of patients were males (64.7%), were <15 years of age (58.8%), and had secondary dystonia as the underlying condition (37.8%). The episodes were mainly characterized by tonic muscle spasms (68.5%), with phasic forms more common in secondary forms and among females. Almost all cases needed a multistaged approach, with surgery being the most successful strategy. Neurological conditions preceding the episode worsened in 16.2% of cases (ending in death in 10.3%). Conclusions: The course and outcome of SD is highly variable; male gender and prevalent tonic phenotype predict a poor outcome.

Affiliations:

France, Hongrie, Inde, Italie, Portugal, Serbie
Latium, Lombardie
Milan, Montpellier, Rome

Links toward previous steps (curation, corpus...)

to stream PascalFrancis, to step Corpus: 000185
to stream PascalFrancis, to step Curation: 002B29
to stream PascalFrancis, to step Checkpoint: 000052
to stream Main, to step Merge: 001031
to stream Main, to step Curation: 000F80
to stream Main, to step Exploration: 000F80
to stream France, to step Extraction: 000112

Links to Exploration step

Pascal:12-0248755

Le document en format XML

<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en" level="a">Status Dystonicus: Predictors of Outcome and Progression Patterns of Underlying Disease</title>
<author><name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
<affiliation wicri:level="3"><inist:fA14 i1="02"><s1>AFaR-Fatebenefratelli Association for Biomedical Research, Neuromed Institute</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Ricciardi, Lucia" sort="Ricciardi, Lucia" uniqKey="Ricciardi L" first="Lucia" last="Ricciardi">Lucia Ricciardi</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
<affiliation wicri:level="1"><inist:fA14 i1="03"><s1>Department of Neurosciences, Psychiatry and Anaesthesiological Science, University of Messina</s1>
<s2>Messina</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<wicri:noRegion>Messina</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Bentivoglio, Anna Rita" sort="Bentivoglio, Anna Rita" uniqKey="Bentivoglio A" first="Anna Rita" last="Bentivoglio">Anna Rita Bentivoglio</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Canavese, Carlotta" sort="Canavese, Carlotta" uniqKey="Canavese C" first="Carlotta" last="Canavese">Carlotta Canavese</name>
<affiliation wicri:level="3"><inist:fA14 i1="04"><s1>Neurological Institute "Carlo Besta</s1>
<s2>Milan</s2>
<s3>ITA</s3>
<sZ>4 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>16 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Zorzi, Giovanna" sort="Zorzi, Giovanna" uniqKey="Zorzi G" first="Giovanna" last="Zorzi">Giovanna Zorzi</name>
<affiliation wicri:level="3"><inist:fA14 i1="04"><s1>Neurological Institute "Carlo Besta</s1>
<s2>Milan</s2>
<s3>ITA</s3>
<sZ>4 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>16 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Petrovic, Igor" sort="Petrovic, Igor" uniqKey="Petrovic I" first="Igor" last="Petrovic">Igor Petrovic</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Kresojevic, Nikola" sort="Kresojevic, Nikola" uniqKey="Kresojevic N" first="Nikola" last="Kresojevic">Nikola Kresojevic</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Kostic, Vladimir S" sort="Kostic, Vladimir S" uniqKey="Kostic V" first="Vladimir S." last="Kostic">Vladimir S. Kostic</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Svetel, Marina" sort="Svetel, Marina" uniqKey="Svetel M" first="Marina" last="Svetel">Marina Svetel</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Kovacs, Norbert" sort="Kovacs, Norbert" uniqKey="Kovacs N" first="Norbert" last="Kovacs">Norbert Kovacs</name>
<affiliation wicri:level="1"><inist:fA14 i1="06"><s1>Department of Neurology, University of Pecs</s1>
<s2>Pecs</s2>
<s3>HUN</s3>
<sZ>10 aut.</sZ>
<sZ>11 aut.</sZ>
</inist:fA14>
<country>Hongrie</country>
<wicri:noRegion>Pecs</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Balas, Istvan" sort="Balas, Istvan" uniqKey="Balas I" first="Istvan" last="Balas">Istvan Balas</name>
<affiliation wicri:level="1"><inist:fA14 i1="06"><s1>Department of Neurology, University of Pecs</s1>
<s2>Pecs</s2>
<s3>HUN</s3>
<sZ>10 aut.</sZ>
<sZ>11 aut.</sZ>
</inist:fA14>
<country>Hongrie</country>
<wicri:noRegion>Pecs</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Roubertie, Agathe" sort="Roubertie, Agathe" uniqKey="Roubertie A" first="Agathe" last="Roubertie">Agathe Roubertie</name>
<affiliation wicri:level="1"><inist:fA14 i1="07"><s1>CHU Montpellier, Hôpital Gui de Chauliac, Service de Neuropédiatrie</s1>
<s2>Montpellier</s2>
<s3>FRA</s3>
<sZ>12 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName><settlement type="city">Montpellier</settlement>
</placeName>
</affiliation>
<affiliation wicri:level="1"><inist:fA14 i1="08"><s1>INSERM U827, Institut Universitaire de Recherche Clinique</s1>
<s2>Montpellier</s2>
<s3>FRA</s3>
<sZ>12 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName><settlement type="city">Montpellier</settlement>
</placeName>
</affiliation>
</author>
<author><name sortKey="Mishra, Devendra" sort="Mishra, Devendra" uniqKey="Mishra D" first="Devendra" last="Mishra">Devendra Mishra</name>
<affiliation wicri:level="1"><inist:fA14 i1="09"><s1>Department of Pediatrics, Maulana Azad Medical College and LN Hospital, University of Delhi</s1>
<s2>Delhi</s2>
<s3>IND</s3>
<sZ>13 aut.</sZ>
</inist:fA14>
<country>Inde</country>
<wicri:noRegion>Delhi</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Mariotti, Paolo" sort="Mariotti, Paolo" uniqKey="Mariotti P" first="Paolo" last="Mariotti">Paolo Mariotti</name>
<affiliation wicri:level="3"><inist:fA14 i1="10"><s1>Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>14 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Temudo, Teresa" sort="Temudo, Teresa" uniqKey="Temudo T" first="Teresa" last="Temudo">Teresa Temudo</name>
<affiliation wicri:level="1"><inist:fA14 i1="11"><s1>Unidade de Neuropediatria, Serviço de Pediatria, Hospital Geral de Santo Antonio</s1>
<s2>Porto</s2>
<s3>PRT</s3>
<sZ>15 aut.</sZ>
</inist:fA14>
<country>Portugal</country>
<wicri:noRegion>Porto</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Nardocci, Nardo" sort="Nardocci, Nardo" uniqKey="Nardocci N" first="Nardo" last="Nardocci">Nardo Nardocci</name>
<affiliation wicri:level="3"><inist:fA14 i1="04"><s1>Neurological Institute "Carlo Besta</s1>
<s2>Milan</s2>
<s3>ITA</s3>
<sZ>4 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>16 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">INIST</idno>
<idno type="inist">12-0248755</idno>
<date when="2012">2012</date>
<idno type="stanalyst">PASCAL 12-0248755 INIST</idno>
<idno type="RBID">Pascal:12-0248755</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">000185</idno>
<idno type="wicri:Area/PascalFrancis/Curation">002B29</idno>
<idno type="wicri:Area/PascalFrancis/Checkpoint">000052</idno>
<idno type="wicri:doubleKey">0885-3185:2012:Fasano A:status:dystonicus:predictors</idno>
<idno type="wicri:Area/Main/Merge">001031</idno>
<idno type="wicri:Area/Main/Curation">000F80</idno>
<idno type="wicri:Area/Main/Exploration">000F80</idno>
<idno type="wicri:Area/France/Extraction">000112</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a">Status Dystonicus: Predictors of Outcome and Progression Patterns of Underlying Disease</title>
<author><name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
<affiliation wicri:level="3"><inist:fA14 i1="02"><s1>AFaR-Fatebenefratelli Association for Biomedical Research, Neuromed Institute</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Ricciardi, Lucia" sort="Ricciardi, Lucia" uniqKey="Ricciardi L" first="Lucia" last="Ricciardi">Lucia Ricciardi</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
<affiliation wicri:level="1"><inist:fA14 i1="03"><s1>Department of Neurosciences, Psychiatry and Anaesthesiological Science, University of Messina</s1>
<s2>Messina</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<wicri:noRegion>Messina</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Bentivoglio, Anna Rita" sort="Bentivoglio, Anna Rita" uniqKey="Bentivoglio A" first="Anna Rita" last="Bentivoglio">Anna Rita Bentivoglio</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Canavese, Carlotta" sort="Canavese, Carlotta" uniqKey="Canavese C" first="Carlotta" last="Canavese">Carlotta Canavese</name>
<affiliation wicri:level="3"><inist:fA14 i1="04"><s1>Neurological Institute "Carlo Besta</s1>
<s2>Milan</s2>
<s3>ITA</s3>
<sZ>4 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>16 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Zorzi, Giovanna" sort="Zorzi, Giovanna" uniqKey="Zorzi G" first="Giovanna" last="Zorzi">Giovanna Zorzi</name>
<affiliation wicri:level="3"><inist:fA14 i1="04"><s1>Neurological Institute "Carlo Besta</s1>
<s2>Milan</s2>
<s3>ITA</s3>
<sZ>4 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>16 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Petrovic, Igor" sort="Petrovic, Igor" uniqKey="Petrovic I" first="Igor" last="Petrovic">Igor Petrovic</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Kresojevic, Nikola" sort="Kresojevic, Nikola" uniqKey="Kresojevic N" first="Nikola" last="Kresojevic">Nikola Kresojevic</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Kostic, Vladimir S" sort="Kostic, Vladimir S" uniqKey="Kostic V" first="Vladimir S." last="Kostic">Vladimir S. Kostic</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Svetel, Marina" sort="Svetel, Marina" uniqKey="Svetel M" first="Marina" last="Svetel">Marina Svetel</name>
<affiliation wicri:level="1"><inist:fA14 i1="05"><s1>Institute of Neurology, Clinical Center of Serbia, School of Medicine</s1>
<s2>Belgrade</s2>
<s3>SRB</s3>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Serbie</country>
<wicri:noRegion>Belgrade</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Kovacs, Norbert" sort="Kovacs, Norbert" uniqKey="Kovacs N" first="Norbert" last="Kovacs">Norbert Kovacs</name>
<affiliation wicri:level="1"><inist:fA14 i1="06"><s1>Department of Neurology, University of Pecs</s1>
<s2>Pecs</s2>
<s3>HUN</s3>
<sZ>10 aut.</sZ>
<sZ>11 aut.</sZ>
</inist:fA14>
<country>Hongrie</country>
<wicri:noRegion>Pecs</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Balas, Istvan" sort="Balas, Istvan" uniqKey="Balas I" first="Istvan" last="Balas">Istvan Balas</name>
<affiliation wicri:level="1"><inist:fA14 i1="06"><s1>Department of Neurology, University of Pecs</s1>
<s2>Pecs</s2>
<s3>HUN</s3>
<sZ>10 aut.</sZ>
<sZ>11 aut.</sZ>
</inist:fA14>
<country>Hongrie</country>
<wicri:noRegion>Pecs</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Roubertie, Agathe" sort="Roubertie, Agathe" uniqKey="Roubertie A" first="Agathe" last="Roubertie">Agathe Roubertie</name>
<affiliation wicri:level="1"><inist:fA14 i1="07"><s1>CHU Montpellier, Hôpital Gui de Chauliac, Service de Neuropédiatrie</s1>
<s2>Montpellier</s2>
<s3>FRA</s3>
<sZ>12 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName><settlement type="city">Montpellier</settlement>
</placeName>
</affiliation>
<affiliation wicri:level="1"><inist:fA14 i1="08"><s1>INSERM U827, Institut Universitaire de Recherche Clinique</s1>
<s2>Montpellier</s2>
<s3>FRA</s3>
<sZ>12 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName><settlement type="city">Montpellier</settlement>
</placeName>
</affiliation>
</author>
<author><name sortKey="Mishra, Devendra" sort="Mishra, Devendra" uniqKey="Mishra D" first="Devendra" last="Mishra">Devendra Mishra</name>
<affiliation wicri:level="1"><inist:fA14 i1="09"><s1>Department of Pediatrics, Maulana Azad Medical College and LN Hospital, University of Delhi</s1>
<s2>Delhi</s2>
<s3>IND</s3>
<sZ>13 aut.</sZ>
</inist:fA14>
<country>Inde</country>
<wicri:noRegion>Delhi</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Mariotti, Paolo" sort="Mariotti, Paolo" uniqKey="Mariotti P" first="Paolo" last="Mariotti">Paolo Mariotti</name>
<affiliation wicri:level="3"><inist:fA14 i1="10"><s1>Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore</s1>
<s2>Rome</s2>
<s3>ITA</s3>
<sZ>14 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Temudo, Teresa" sort="Temudo, Teresa" uniqKey="Temudo T" first="Teresa" last="Temudo">Teresa Temudo</name>
<affiliation wicri:level="1"><inist:fA14 i1="11"><s1>Unidade de Neuropediatria, Serviço de Pediatria, Hospital Geral de Santo Antonio</s1>
<s2>Porto</s2>
<s3>PRT</s3>
<sZ>15 aut.</sZ>
</inist:fA14>
<country>Portugal</country>
<wicri:noRegion>Porto</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Nardocci, Nardo" sort="Nardocci, Nardo" uniqKey="Nardocci N" first="Nardo" last="Nardocci">Nardo Nardocci</name>
<affiliation wicri:level="3"><inist:fA14 i1="04"><s1>Neurological Institute "Carlo Besta</s1>
<s2>Milan</s2>
<s3>ITA</s3>
<sZ>4 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>16 aut.</sZ>
</inist:fA14>
<country>Italie</country>
<placeName><settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
</analytic>
<series><title level="j" type="main">Movement disorders</title>
<title level="j" type="abbreviated">Mov. disord.</title>
<idno type="ISSN">0885-3185</idno>
<imprint><date when="2012">2012</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt><title level="j" type="main">Movement disorders</title>
<title level="j" type="abbreviated">Mov. disord.</title>
<idno type="ISSN">0885-3185</idno>
</seriesStmt>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Dystonia</term>
<term>Midazolam</term>
<term>Nervous system diseases</term>
<term>Pantothenate kinase</term>
<term>Prognosis</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr"><term>Dystonie</term>
<term>Pathologie du   système nerveux</term>
<term>Pronostic</term>
<term>Midazolam</term>
<term>Pantothenate kinase</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">Background: Status dystonicus (SD) is a rare, lifethreatening disorder characterized by acute worsening of generalized dystonia. Methods: This study was conducted to characterize the pathogenesis, clinical course, and prognosis of SD. We reviewed the records of six centers and analyzed them together with all the cases previously reported in the literature. Results: Eighty-nine episodes occurring in 68 patients were studied. The majority of patients were males (64.7%), were <15 years of age (58.8%), and had secondary dystonia as the underlying condition (37.8%). The episodes were mainly characterized by tonic muscle spasms (68.5%), with phasic forms more common in secondary forms and among females. Almost all cases needed a multistaged approach, with surgery being the most successful strategy. Neurological conditions preceding the episode worsened in 16.2% of cases (ending in death in 10.3%). Conclusions: The course and outcome of SD is highly variable; male gender and prevalent tonic phenotype predict a poor outcome.</div>
</front>
</TEI>
<affiliations><list><country><li>France</li>
<li>Hongrie</li>
<li>Inde</li>
<li>Italie</li>
<li>Portugal</li>
<li>Serbie</li>
</country>
<region><li>Latium</li>
<li>Lombardie</li>
</region>
<settlement><li>Milan</li>
<li>Montpellier</li>
<li>Rome</li>
</settlement>
</list>
<tree><country name="Italie"><region name="Latium"><name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
</region>
<name sortKey="Bentivoglio, Anna Rita" sort="Bentivoglio, Anna Rita" uniqKey="Bentivoglio A" first="Anna Rita" last="Bentivoglio">Anna Rita Bentivoglio</name>
<name sortKey="Canavese, Carlotta" sort="Canavese, Carlotta" uniqKey="Canavese C" first="Carlotta" last="Canavese">Carlotta Canavese</name>
<name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
<name sortKey="Mariotti, Paolo" sort="Mariotti, Paolo" uniqKey="Mariotti P" first="Paolo" last="Mariotti">Paolo Mariotti</name>
<name sortKey="Nardocci, Nardo" sort="Nardocci, Nardo" uniqKey="Nardocci N" first="Nardo" last="Nardocci">Nardo Nardocci</name>
<name sortKey="Ricciardi, Lucia" sort="Ricciardi, Lucia" uniqKey="Ricciardi L" first="Lucia" last="Ricciardi">Lucia Ricciardi</name>
<name sortKey="Ricciardi, Lucia" sort="Ricciardi, Lucia" uniqKey="Ricciardi L" first="Lucia" last="Ricciardi">Lucia Ricciardi</name>
<name sortKey="Zorzi, Giovanna" sort="Zorzi, Giovanna" uniqKey="Zorzi G" first="Giovanna" last="Zorzi">Giovanna Zorzi</name>
</country>
<country name="Serbie"><noRegion><name sortKey="Petrovic, Igor" sort="Petrovic, Igor" uniqKey="Petrovic I" first="Igor" last="Petrovic">Igor Petrovic</name>
</noRegion>
<name sortKey="Kostic, Vladimir S" sort="Kostic, Vladimir S" uniqKey="Kostic V" first="Vladimir S." last="Kostic">Vladimir S. Kostic</name>
<name sortKey="Kresojevic, Nikola" sort="Kresojevic, Nikola" uniqKey="Kresojevic N" first="Nikola" last="Kresojevic">Nikola Kresojevic</name>
<name sortKey="Svetel, Marina" sort="Svetel, Marina" uniqKey="Svetel M" first="Marina" last="Svetel">Marina Svetel</name>
</country>
<country name="Hongrie"><noRegion><name sortKey="Kovacs, Norbert" sort="Kovacs, Norbert" uniqKey="Kovacs N" first="Norbert" last="Kovacs">Norbert Kovacs</name>
</noRegion>
<name sortKey="Balas, Istvan" sort="Balas, Istvan" uniqKey="Balas I" first="Istvan" last="Balas">Istvan Balas</name>
</country>
<country name="France"><noRegion><name sortKey="Roubertie, Agathe" sort="Roubertie, Agathe" uniqKey="Roubertie A" first="Agathe" last="Roubertie">Agathe Roubertie</name>
</noRegion>
<name sortKey="Roubertie, Agathe" sort="Roubertie, Agathe" uniqKey="Roubertie A" first="Agathe" last="Roubertie">Agathe Roubertie</name>
</country>
<country name="Inde"><noRegion><name sortKey="Mishra, Devendra" sort="Mishra, Devendra" uniqKey="Mishra D" first="Devendra" last="Mishra">Devendra Mishra</name>
</noRegion>
</country>
<country name="Portugal"><noRegion><name sortKey="Temudo, Teresa" sort="Temudo, Teresa" uniqKey="Temudo T" first="Teresa" last="Temudo">Teresa Temudo</name>
</noRegion>
</country>
</tree>
</affiliations>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/MovDisordV3/Data/France/Analysis

HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 000112 | SxmlIndent | more

HfdSelect -h $EXPLOR_AREA/Data/France/Analysis/biblio.hfd -nk 000112 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Wicri/Santé
   |area=    MovDisordV3
   |flux=    France
   |étape=   Analysis
   |type=    RBID
   |clé=     Pascal:12-0248755
   |texte=   Status Dystonicus: Predictors of Outcome and Progression Patterns of Underlying Disease
}}

This area was generated with Dilib version V0.6.23.
Data generation: Sun Jul 3 12:29:32 2016. Site generation: Wed Feb 14 10:52:30 2024

	Movement Disorders (revue)
	Attention, ce site est en cours de développement ! Attention, site généré par des moyens informatiques à partir de corpus bruts. Les informations ne sont donc pas validées.

Movement Disorders (revue)

Status Dystonicus: Predictors of Outcome and Progression Patterns of Underlying Disease

Status Dystonicus: Predictors of Outcome and Progression Patterns of Underlying Disease

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri